All issues > Volume 33(6); 1990

Original Article

J Korean Pediatr Soc. 1990;33(6):830-834. Published online June 30, 1990.

A Case of Congenital Cystic Adenomatoid Malformation (Type1) of the Lung.

Dong Sik Kim¹, Hwang Min Kim¹, Jae Seung Yang¹, Baek Keun Kim¹, Jong Soo Kim¹, Dong Hwan Shin²

¹Department of Pediatrics, Yonsei University, Wonju College of Medicine
²Department of Pathology, Yonsei University, Wonju College of Medicine

Correspondence Dong Hwan Shin ,

Received: January 15, 1990;  Accepted: March 23, 1990.

Abstract

A rare form of congenital cystic lung disease, characterized by the presence of one or usually multiple interconnecting cyst, is called congenital cystic adenomatoid malformation of the lung. This disease almost invariably presents either in live premature or stillborn infants, and death in those infants bom alive usually occurs within a few hours of birth. Infants with congenital cystic adenomatoid malformation usually have tachypnea, cyanosis, and other forms of respiratory distress at or shortly after birth. These manifestations are related to expansion of the cysts with resultant compression of the remaining normal lung. We have experienced a case of cystic adenomatoid malformation (Type I) of the lung in 10 months old female infant who had frequent upper respiratory tract infection and respiratory distress. A brief review of the related literature is presented.

Keywords :Congenital Cystic Adenomatoid Malformation, Congenital Cystic Lung Disease