All issues > Volume 33(5); 1990

Original Article

J Korean Pediatr Soc. 1990;33(5):684-689. Published online May 31, 1990.

A Case of Pancreatoblastoma with Metastasis of the Liver.

Dae Sung Oh¹, Yong Won Paik¹, Jae Sun Park¹, Kyung Hyun Choi², Man Ha Huh³

¹Department of Pediatrics, Kosin Medical College, Pusan, Korea
²Department of General Surgery, Kosin Medical College, Pusan, Korea
³Department of Pathology, Kosin Medical College, Pusan, Korea

Received: October 20, 1989;  Accepted: November 10, 1989.

Abstract

We experenced a case of pancreatoblastoma in a 6 years old Korean male who was admmited to the pediatric department because of an abdominal mass and pathologically diagnosed following surgical removal. Microscopically, the resected mass was composed of small sized tumor cells arranged in glandular or acini structure with multifoci of squamoid corpuscle. Extensive hemorrhagic necrosis was another feature. Ultrastructucturally, two types of cells, dark and clear, were seen as component cells of the tumor. Microvilli and elctron dense zymogen-like granules were seen. Wipple*s operation was done. Hepatic metastasis were detected two times radiologically at 7 month and 34 month after first complete resection and each metastasis was following by remission with chemotherapy and/or partial hepatic resection. The patient is alive for 17 months after third remis- sion. The review of literatures was made briefly.

Keywords :Pancreatoblastoma, Liver metastasis