All issues > Volume 33(2); 1990

Original Article

J Korean Pediatr Soc. 1990;33(2):229-233. Published online February 28, 1990.

2 Case of Scimitar syndrome.

Jae Kon Ko¹, Nam Su Kim¹, Woong Heum Kim¹, Heung Jae Lee¹, Shi Joon Yoo²

¹Department of Pediatrics, Sejong General Hospital
²Department of Radiology, Sejong General Hospital

Received: June 9, 1989;  Accepted: September 10, 1989.

Abstract

The scimitar syndrome, a rare complex anomaly, consists essentially of an anomalous pulmonary vein draining whole or part of right lung into inferior vena cava and its curved Turkish sword (scimitar) like appearance has provided the name of this syndrome. Associated anomalies are frequent, such as hypoplasia of the right lung and right pulmonary artery, abnormalities of bronchial architecture and lobation, rightward displacement of heart and systemic arterial supply to the right lung. Other congenital cardiac abnormalities are associated with about 25% of this syndrome. We have experienced 2 cases of the scimitar syndrome in infant and 12year old boy recently, so we presented with a brief review of the literatures.

Keywords :Scimitar syndrome