All issues > Volume 32(12); 1989

Original Article

J Korean Pediatr Soc. 1989;32(12):1752-1756. Published online December 31, 1989.

A Case of Hydranencephaly.

Min Cheol Kim¹, Moon Ja Park¹, Kong Sik Kim¹, Kyeong Rae Moon¹, Yeong Bong Park¹

¹Department of pediatrics, College of Medicine, Chosun University, Gwangju, Korea

Received: May 29, 1989;  Accepted: August 14, 1989.

Abstract

Hydranencephaly is congenital absence of the cerebral hemispheres, which are replaced by a large, fluid-filled cavity. The brain stem and basal ganglia are well formed, and rudients of frontal & occipital cortex may be present. We experienced a cases of hydranencephaly in a 6 month-old male infant who had not haven visual following and head control. We diagnosed it through the evaluation of clinical features, skull transillumination and brain CT. A brief review of the related literatures was made.

Keywords :Hydranencephaly