All issues > Volume 32(7); 1989

Original Article

J Korean Pediatr Soc. 1989;32(7):995-1000. Published online July 31, 1989.

A Case of Cytophagic Histiocytic Panniculitis.

Hyung Keun Nam¹, Byong Rai Cho¹, Don Hee Ahn¹, Keun Chan Sohn¹, Jin Hee Sohn²

¹Department of Pediatrics, National Medical Center, Seoul, Korea
²Department of Pathology, National Medical Center, Seoul, Korea

Received: November 20, 1988;  Accepted: December 24, 1988.

Abstract

Cytophagic histiocytic panniculitis is a chronic, benign, visceral and cutaneous histiocytic (cyto- phagic) paniculitis, progressing to liver dysfunction, jaundice and a terminal hemorrhagic diathesis. We have experienced a case of cytophagic histiocytic panniculitis in an 11 year old male who had developed recurrent fever and subcutaneous nooules since infancy, progressing to liver dysfunction, jaundice and hemorrhagic diathesis. The noaular biopsy also showed a characteristic histiocytic panniculitis, such as bean bag cell. A brief review of literatures was made.

Keywords :Cytophagic histiocytic panniculitis, Terminal bleeding diathesis, Bean bag cell