All issues > Volume 32(7); 1989

Original Article

J Korean Pediatr Soc. 1989;32(7):990-994. Published online July 31, 1989.

A Case of Peutz-Jeghers Syndrome.

Ick berm Park¹, Sung guen Oh¹, Jung suk Ko¹, Sang hyun Byun¹, Kyu chul Choeh¹

¹Department of Pediatrics, Eul Ji General Hospital, Dae Jeon, Korea

Received: November 26, 1988;  Accepted: December 20, 1988.

Abstract

This is a report of our experience of Peutz-Jeghers syndrome in a 14 year old girl having family history. She was admitted with complaints of crampy abdominal pain and vomiting, and showed melanotic pigmentation on the lips, face around nose, oral mucosa around molar areas, fingers and toes. Colon study revealed multiple polyposis in colon and small bowel. In family, her father has melanotic pigmentation and a history of operation for intestinal polyposis. And her younger brother has melanotic pigmentation but has not yet developed intestinal symptoms.

Keywords :Peutz-Jeghers syndrome, Melanotic pigmentation, Polyposis