All issues > Volume 31(10); 1988

Original Article

J Korean Pediatr Soc. 1988;31(10):1358-1365. Published online October 31, 1988.

Three Cases of Single Ventricle with Asplenia.

Bong Shin Lee¹, Yoo Ho Kim¹, Byoung Hai Ahn¹, Young Hee Yoo¹, Hyun Suk Lee¹, Jeong Rye Kim², Wook Younm³

¹Department of Pediatrics, Korean Veterans Hospital, Seoul, Korea
²Department of Anatomical Pathology, Korean Veterans Hospital, Seoul, Korea
³Department of Thoracic Surgery, Korean Veterans Hospital, Seoul, Korea

Received: April 9, 1988;  Accepted: April 9, 1988.

Abstract

Congenital asplenia syndrome is associated with malposition and malformation of other organ system such as congenital heart disease, patial or complete situs inversus, symmetric lobulation of the liver and the lung. This is a rare syndrome but has been reported in increaseing frequency in recent years. We experienced three cases of this single ventricle with asplenia. One is confirmed by autopsy and the others are diaqnosed by other methods Literatures were reviewed briefly.

Keywords :Single ventricle with asplenia