All issues > Volume 31(6); 1988

Original Article

J Korean Pediatr Soc. 1988;31(6):790-795. Published online June 30, 1988.

Hypoplastic Left Heart Syndrome : Report of a Unique Survivor.

Hang Bo Cho¹, Seong Ho Kim¹, Ha Baik Lee¹, Kyu Hwang Rhee¹, Chong Moo Park¹

¹Department of Pediatrics, College of Medicine, Hanyang University, Seoul, Korea

Received: November 24, 1987;  Accepted: January 21, 1988.

Abstract

Hypoplastic left heart syndrome is a rare, and fatal congenital heart disease. Most of the patients with this syndrome die within the 1st month of life. Recently we experienced a hypoplastic left heart syndrome in a child who was unusually living without surgical intervention for 3 and half years. The unique clinical course might result from a number of favorable hemodynamic factors and intact ventricular septum 1) widely patent ductus arteriosus, 2) adequate coronary flow from narrow ascending aorta, 3) unrestricted pulmonary venous return, and 4) absence of significant vascular obstructive disease. In addition to the case report, a review of recent literatures was made.

Keywords :Hypoplastic left heart syndrome