All issues > Volume 31(4); 1988

Original Article

J Korean Pediatr Soc. 1988;31(4):500-505. Published online April 30, 1988.

Three Cases of hereditary Spherocytosis.

D H Kim¹, M Y Kim¹, S Y Kim¹, J Y Jung¹

¹Department of Pediatrics, Hae Sung Hospital

Received: July 12, 1987;  Accepted: December 2, 1987.

Abstract

We experienced 3 cases of herediatry spherocytosis which occurred in a family. The family consited of parents, one sone and one daughter. The case I, Daughter showed the chief complaints of pallor ad generalized weakness. The case II, Son hoswed the chief complaint of jaundice. The case III, Father showed the chief complaints of fatigue and dizziness. Diagnosis was made by presence of spherocytes in peripheral blood smear, osmotic fragility test, autohemolysis test, and bone marrow examination. All 3 patiens were treated by splenectomy, after which symptomatic improvements were very remarkable. A brief review of related literature was made.

Keywords :Hereditary Spherocytosis