All issues > Volume 31(3); 1988

Original Article

J Korean Pediatr Soc. 1988;31(3):398-403. Published online March 31, 1988.

A Case of Kasabach-Merritt Syndrome.

S H Lee¹, S J Kim¹, H D Cha¹, T W Paik¹, C M Kang¹

¹Department of Pediatrics, Keimyung University, School of Medicine, Taegu, Korea

Received: November 18, 1987;

Abstract

Kasabach-Merritt syndrome (Giant hemangioma associated with thrombo-cytopenia) is a rare disease in infants and ifs hemorrhgic manifestations in these patients are frequently severe enough to threaten life. We experienced a case of this syndrome in a 19 days old boy who had a huge hemangioma on the left upper arm, left anterior chest and back, associated with thrombocytopenia at birth. The patient also had pneumonia of left mid lung and pleural effusion on admission. The hemangioma had progressed rapidly after admission and developed continuous bleeding from the mass in spite of the transfusion of platelet concentrates. He expired on the 3rd hospital day for pneumonia and bleeding. Brief review of the literature was made.

Keywords :Kasabach-Merritt syndrome