All issues > Volume 30(11); 1987

Original Article

J Korean Pediatr Soc. 1987;30(11):1282-1286. Published online November 30, 1987.

A Case of Potter Syndrome with Bilateral Polycystic Kidneys.

Chun Hwa Lee¹, Jung Hwan Choi¹, Yong Choi¹, Chong Ku Yun¹, Yeon Lim Suh², Je G Chi², Son Moon Shin³

¹Department of Pediatrics, College of Medicine, Seoul- National University
²Department of Pathology, College of Medicine, Seoul- National University
³Department of Pediatrics, College of Medicine, Young Nam Univerity

Abstract

In 1946, Potter described a series of 20 cases of infants in whom bilateral absence of the kidneys was associated with hypoplasia of the lungs and characteristic faces. Afterwards it has been known that any condition that causes significant reduction in urine formation or excretion will result in oligohydramnios accounts for many of the nonrenal features of Potter syndorme. We report a case of Potter syndrome with bilateral polycystic renal dysplasia and add a brief review of literatures.

Keywords :Potter syndrome; Oligohydramnios;Hypoplastic lung;Polycystic renal dysplasia.