All issues > Volume 30(10); 1987

Case Report

J Korean Pediatr Soc. 1987;30(10):1176-1181. Published online October 31, 1987.

A Case of Cor triatrium Dexter.

Hong Kun Kim¹, Sung Oh Kim¹, Kyoo Hwan Rhee¹

¹Department of Pediatrics, School of Medicine, Hanyang University, Seoul, Korea

Abstract

Cor triatrium dexter is a rare congenital anomaly, in which persistent Rt. side valve of sinus venosus subdivides the Rt. atrium into two chambers. Although this lesion was described earlier by Rokitansky, et al, the term “Cor triatrium dexter” was coined by German pathologists in the beginning of this century. The most cases of the Cor triatrium dexter are due to persistence of fetal Eustachian & Thebesian valves which form a septum across the lower part of the right atrium. Most of the patients with this anomaly are usually asymptomatic unless associated with other congenital cardiac anomaly. Therefore it may not be possible to find a clinical account of isolated Cor triatrium dexter. We have experienced a 22 months-old girl who had an excessive membranous septum in the right atrium associated with a severe valvular pulmonary stenosis and a right to left shunt at the atrial level. A brief review of related literatures is given.

Keywords :Cor triatrium dexter