All issues > Volume 30(8); 1987

Original Article

J Korean Pediatr Soc. 1987;30(8):916-921. Published online August 31, 1987.

Two Cases of Congenital Asplenia.

Man Chul Ha¹, Young Tak Lim¹, Hi Joo Chun¹, Hi Ju Park¹, Chan Yung Kim¹

¹Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea

Abstract

Congenital absence of spleen is often associated with malpositions and malformations of other organ system such as congenital heart disease partial situs inversus, symmetric lobulation of the liver and the lungs. This is a rare syndrome but has been reported in increasing frequency in recent years. The pure congenital asplenia is a very rare disease. We experienced two cases of congenital asplenia. One is a pure congenital asplenia and the other is an asplenia associated with congenital heart disease and partial situs inversus. The review of the literature was made briefly.

Keywords :Pure congenital asplenia and asplenia syndrome associated congenital cardiac malforma- tions and partial situs inversus.