All issues > Volume 30(7); 1987

Case Report

J Korean Pediatr Soc. 1987;30(7):812-817. Published online July 31, 1987.

A Case of Potter Syndrome Associated with Renal Dysplasia.

Young Woo Park¹, Joon Ho Kim¹, Eun Ryoung Kim¹, Soon Jae Lee¹, Young Chul Moon¹, Young Jin Kim²

¹Department of Pediatrics, Sung Ae Hospital, Seoul, Korea
²Department of Pathology, Sung Ae Hospital, Seoul, Korea

Abstract

Potter syndrome is relatively rare congenital defect in with agenesis or dysplasia of the kidney is associated with oligohydramnios, pulmonary hypoplasia, characteristic facial features and other abnormalities. The etiology is unknown. But various theories are reviewed and the suggestion is made that the cause of Potter syndrome in newborns may well be multifactorial. Among the various factors, we agree to the opinion that oligohydramnios and multifocal primary mesodermal defect may be the cause of Potter syndrome. In rescent day, prenatal diagnosis of Potter syndrome is possible by means of ultrasound scanning and many other methods. We reported a case of Potter syndrome associated with renal dysplasia and a brief review of the literature was made.

Keywords :Potter syndrome; Renal dysplasia.