All issues > Volume 30(4); 1987

Original Article

J Korean Pediatr Soc. 1987;30(4):422-426. Published online April 30, 1987.

A Case of Pulmonary Lymphangiectasis Associated with Chylothorax.

Min Hee Kim¹, Jae Kyoung Lee¹, Oh Bae Chun¹, Byoung Hoon Yoo¹, Jae Hyung Yoo²

¹Department of Pediatrics, College of Medicine, Chung Ang University, Seoul, Korea
²Department of Pathology, College of Medicine, Chung Ang University, Seoul, Korea

Abstract

Congenital pulmonary lymphangiectasis is a rare abnormality usually becoming manifest at birth and almost invariably fatal in neonatal period or early infancy. Chylothorax is an infrequent manifestation of this disease. We report a patient with pulmonary lymphangiectasis, 3 year old male, who had been suffered from persistent respiratory distress since 7 days after birth, in whom the diagnosis was suggested by the appearance of chylothorax and confirmed by open lung biopsy. He died of pulmonary failure 4 months after discharge.

Keywords :Pulmonary lymphangiectasis ; Chylothorax.