All issues > Volume 30(3); 1987

Case Report

J Korean Pediatr Soc. 1987;30(3):314-319. Published online March 31, 1987.

A Case of Distal Type of Renal Acidosis.

Han young Jeong¹, Soon Yol Whang¹, Sung Won Kim¹, Kyung Tae Kim¹, Kil Hyun Kim¹

¹Department of Pediatrics, St. Benedict Hospital, Busan, Korea

Abstract

A 5 years old girl was admitted to Ped. Dept, of St. Benedict Hospital due to pneumonia, gait disability and knock knee. Physical examination on admission showed a picture of full blown rickets such as poor development, waddling gait, knock knee, widening of both wrists, rachitic rosary and compatible X-ray picture. IVP showed bilateral nephrocalcinosis with normal excretory function. Laboratory data showed hypematremin, hyperchloremia, hypokalemia and high alkaline phosphatase level. Blood gas analysis showed severe metabolic acidosis In spite of these data, urine pH was above 6.0. Under the impression of renal tubular acidosis (distal type), alkali therapy with NaHCO3 and potassium supplement were done. After 2 weeks of treatment, marked improvement was noted both in clinical symptoms and laboratory results. With the review of literatures, the case is presented.

Keywords :Renal tubular acidosis, Distal type.