All issues > Volume 30(2); 1987

Original Article

J Korean Pediatr Soc. 1987;30(2):218-222. Published online February 28, 1987.

A Case of Congenital Asplenia Syndrome.

Hyung Sook Kim¹, Jin Soo Cho¹, Sung Kee Jim¹, Doo Sung Moon¹, kyung Sook Cho¹, Jong Dae Cho¹

¹Department of Pediatries, Maliknol Hospital

Abstract

Department of Pediatrics, Maliknol Hospital The congenital asplenia syndrome is very rarely seen and is characterized by congenital absence of the spleen, usually associated with other groups of cardio-vascular, bronchopulmonary and gastrointestinal tract. The authors recently experienced a case of congenital asplenia syndrome in a 6 month-old, male infant. He has no splenic image by using 99m Technetium-sulfur scanning. He also had common atrioventricular canal, ventricular septal defect, transposition of great arteries and pulmonary stenosis in the two dimensional echocardiographic study.

Keywords :Asplenia syndrome.