All issues > Volume 30(2); 1987

Original Article

J Korean Pediatr Soc. 1987;30(2):207-211. Published online February 28, 1987.

Pheochromocytoma in Two 10-year Old Children.

Young Soo Kim¹, Young Hoon Kim¹, Se Won Yang¹, Yong Choi¹, Hyung Ro Moon¹

¹Department of Pediatrics, College of Medicine, Seoul National University

Abstract

We experienced two cases of pheochromocytoma in 10 year-old boy and girl. Boy had bilateral and girl had unilateral pheochromocytoma. Both patients who were severely retarded in height growth had hypertension and one patient had cardiomyopathy. In both patients, vanillylmandelic acid in urine was increased, and phentolamine test was positive. Adrenal mass was visualized by C.T. in each ease. Successful surgical removal was done, and both patients have been in normal B.P. till now without subjective symptoms. The authors stress that short stature is one of the characteristic physical findings if pheochromocytoma in early childhood.

Keywords :Pheochromocytoma, Hypertension, Cardiomyopathy, Vanillylmandelic acid, Growth retardation.