All issues > Volume 29(12); 1986

Case Report

J Korean Pediatr Soc. 1986;29(12):1387-1392. Published online December 31, 1986.

A Case of Nesidioblastosis.

M J Kim¹, K S Choi¹, H D Cha¹, C M Kang¹, W H Park²

¹Department of Pediatrics, Keimyung University School of Medicine, Taegu, Korea
²Department of Pediatric Surgery, Keimyung University School of Medicine, Taegu, Korea

Abstract

Nesidioblastosis is an extremely rare disorder of unknown origin, resulted from inappropriate control of early development of endocrine pancreas. The authors experienced a case of nesidioblastosis, in a 1 day old male neonate whose blood sugar was 3mg/dl at birth and hypoglycemia had persisted thereafter.Near total pancreatectomy was done and diagnosis was confirmed by histologic findings of biopsied specimen. A brief review of related literature was made,.

Keywords :Nesidioblastosis; Pancreatectomy. -