All issues > Volume 29(11); 1986

Case Report

J Korean Pediatr Soc. 1986;29(11):1275-1280. Published online November 30, 1986.

A Case of Dubin-Johnson Syndrome in Childhood.

Young Hoon Kim¹, Young Soo Kim¹, Sang Kyu Park¹, Jung Ki Seo¹, Yong Choi¹

¹Dept, of Pediatrics, College of Medicine, Seoul National University

Abstract

A case of Dubin-Johnson syndrome in 10-year-old Korean male child was presented. The presenting symptom was dark-colored urine for several years. Laboratory findings showed increased bilirubin, especially direct-reacting bilirubin, and abnormal urinary coproporphyrin pattern (coproporphyrin I : 58%, coproporphyrin JK : 42%). Needle biopsy specimen of liver showed dark-brownish pigmentation in liver cells but was otherwise normal histologically.

Keywords :Dubin-Johnson syndrome.