All issues > Volume 29(10); 1986

Case Report

J Korean Pediatr Soc. 1986;29(10):1152-1156. Published online October 31, 1986.

A Case of Potter Syndrome Type I.

Jong Cheol Ryu¹, Jae Kwang Hong¹, Jun Taek Park¹, Jung Sik Min¹, Chang Jee Choi¹, Je Geun Chi²

¹Department of Pediatrics, Seoul Adventist Hospital
²Department of Pathology, Seoul National University

Abstract

We have experienced a case of Potter syndrome type I in a newborn infant who presented with severe respiratory distress soon after birth. The diagnosis was made with autopsy findings consisted of bilateral polycystic renal dysplasia, bilateral hypoplastic lung , facies renalis, fibrocystic change of liver, patent ductus arteriosus, patent foramen ovale, ureter and urinary bladder hypoplasia and calcaneovarus. Brief reviews of the related literatures are given.

Keywords :Potter syndrome type I; Facies renalis;Hypoplastic lung; Polycystic renal dysplasia.