All issues > Volume 29(8); 1986

Case Report

J Korean Pediatr Soc. 1986;29(8):918-923. Published online August 31, 1986.

A Case of Prune Belly Syndrome.

Gyu Ho Lim¹, Kyung Ja Lee¹, Woo Kap Chung¹

¹Department of Pediatrics, Chunchon Sacred Heart Hospital, Kangwon, Korea

Abstract

Prune belly syndrome is a very rare congenital anomaly characterized by congenital deficiency of the abdominal muscle wall and wrinkled irregular skin, prune like in appearance. It has been referred to as triad syndrome because three major features are seen in most cases: deficiency of the abdominal muscle wall, hydroureter and hydronephrosis, and cryptochidism. We report a rare case of prune belly syndrome in a 6-year-old male child and review the literature.

Keywords :Prune belly syndrome.