All issues > Volume 29(3); 1986

Case Report

J Korean Pediatr Soc. 1986;29(3):327-331. Published online March 31, 1986.

A Case of Pulmonary Arteriovenous Fistulas with Cyanosis.

Yun Oak Rho¹, Hyun Eog Yang¹, Kyong Su Lee¹, Kyung Sub Shin²

¹Department of Pediatrics, Catholic Medical College, Seoul, Korea
²Department of Radiology, Catholic Medical College, Seoul, Korea

Abstract

Pulmonary arteriovenous fistula is a congenital vascular malformation in lung resulting from abnormal capillary development and thus unoxygenated, desaturated arterial blood enters into the pulmonary venous system and results in various symptoms such as exertional dyspnea, cyanosis, clubbing fingers and secondary polycythemia. The exact etiology of pulmonary arteriovenous fistula is not well known but it may occur with or without hereditary hemorrhagic telangiectasia(Rendu-Osler-Weber syndrome). Pulmonary arteriovenous fistula often goes unrecognized early in life. Recently we experienced a case of the pulmonary arteriovenous fistulas in 15 years old boy, which was confirmed by cardiac catheterization and pulmonary arteriography preoperatively. Left lower lobectomy and lingular wedge resection were performed. Postoperative physiological studies showed nearly normal oxygen saturation, Hb and Rbc count. The patient had a good postoperative course and discharged.

Keywords :Pulmonary arteriovenous fistulas