All issues > Volume 28(10); 1985

Case Report

J Korean Pediatr Soc. 1985;28(10):1032-1036. Published online October 31, 1985.

A Case of Letter-Siew Disease.

Yoon Ho Kang¹, Suck Young Lee¹, Jin Sook Lee¹, Kwang Ho Kim¹, Soo Nam Lee²

¹Department of Pediatrics, Inchon Christian Hospital, Inchon,Korea
²Department of Pathology, Inchon Christian Hospital, Inchon,Korea

Abstract

A case of Letterer-Siwe disease in a 6 month-old Korean male manifesting maculopapular skin rash, watery diarrhea, fever and bony skull defect as classical features of the disease was presented. The diagnosis was confirmed by clinical symptoms, histopathologic and radiologic findings. The authors report a fatal case which was treated in hospital with intensive antibiotics, corticosteroid and alkylating agent.

Keywords : Letterer-Siwe disease