All issues > Volume 28(8); 1985

Case Report

J Korean Pediatr Soc. 1985;28(8):795-800. Published online August 31, 1985.

A Case of Unilateral Lung Agenesis (Right) Associated with Skeletal Anomalies.

Woan Chul Suh, Dong Youl Lee, Kyung Ae Lee, Hee Ju Kim, Sung Ill Ahn, Bom Woo Yeom

¹Department of Pediatrics,Seoul Eul Ji General Hospital, Seouly Korea
²Department of Clinical Pathology,Seoul Eul Ji General Hospital, Seouly Korea

Abstract

Lung agenesis is defined as total absence of pulmonary parenchyma with its supporting vasculature, as well as the main stem bronchi on one or both sides. This anomaly is usually associated with extrapulmonary anomalies such as cardiac, vascular, gastrointestinal, skeletal, genitourinary, and miscellaneous anomalies. We experienced a case of unilateral lung agenesis(Right) in a three days old female premature baby, who admitted to our hospital with chief complaints of cyanosis on feeding and respiratory difficulty. The diagnosis was established by physical examination, chest X-ray, EKG, lung perfusion scan, and confirmed by autopsy. Associated anomalies were fusion anomaly between T12 & Ll, midline cleft on Ll & L2 and accessory rudimentary thumb on right hand. The review of literature was made briefly.

Keywords :Unilateral lung agenesis; Skeletal anomalies