All issues > Volume 28(2); 1985

Case Report

J Korean Pediatr Soc. 1985;28(2):191-196. Published online February 28, 1985.

A case of Infantile Polycystic kidney.

Ae Sook Kim, Soon Bock Park, Young Gun Kim, Kwan Hwooy Cho, Jong Soo Kim

¹Department of Pediatrics, Wonju College of Medicine,Yonsei University

Abstract

Infantile polycystic kidney is uncommon disease and rare in children and is used to refer to a group of heritable conditions that occur predominantly in childhood and is transmitted by autosomal recessive inheritance. By developmental abnormality, multiple cysts are produced from enlargement or giantism of the collecting tubules in association with cellular hyperplasia. Kidneys are grossly enlarged and have a diffusely spongy appearence due to innumerable, radially arranged, fusiform cysts. This paper presented a case of bilateral infantile polycystic kidney in 20 day-old male baby is presented. He has respiratory distress, abdominal distension. The diagnosis of infantile polycystic kidney was made by I.V.P.

Keywords :Infantile polycystic kidney