All issues > Volume 27(11); 1984

Case Report

J Korean Pediatr Soc. 1984;27(11):1113-1117. Published online November 30, 1984.

A Case of Congenital Asplenia Associated with Congenital Cardiac Malformation and Partial Situs Inversus.

Jung Sim Choi¹, Yoon Ho Kang¹, Sook Young Lee¹, Jin Sook Lee¹, Kawng Ho Kim¹, Soo Nam Lee²

¹Department of Pediatrics，Inchon Christian Hospital，Inchon, Korea
²Department of Clinical Pathology，Inchon Christian Hospital，Inchon, Korea

Abstract

The postmortem finding in a 64 day-old Korean male of asplenia associated with congenital malformation of heart and partial situs inversus of the abdominal viscera has been presented. And results were as follows. 1. Heart 1) abscence of atrial septum with, triangular muscular band. 2) common atrioventricular orfice with, anomalous attachment. 3) univentricle. 2. Respiratory tract 1) bilateral trilobed lung. 2) chronic passive congestion of lung, bilateral. 3. Gastrointestinal tract 1) Right sided stomach, duodenum and pancreas. 2) Enlarsgment of left lobe of liver. 4. Abscence of spleen

Keywords :Congenital asplenia; Congenital cardiac malformation; Partial situs inversus.