All issues > Volume 27(8); 1984

Case Report

J Korean Pediatr Soc. 1984;27(8):814-819. Published online August 31, 1984.

A Case of Isolated Congenital Tricuspid Insufficiency.

Dong Hyun Choo, Dong Kyoon Kim, Jung Yeon Choi, Yong Soo Yoon, Chang Yee Hong

¹Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea

Abstract

Isolated congenital tricuspid insufficiency is a rare anomaly and may be caused by abnormal chordae tendinae, papillary muscle, or valve leaflets. The cause of these lesions is generally ascribed to incomplete undermining of primitive endocardial cushion by sinusoidal space, which differentiate the cushion into the various valvular structures. Carvallo’s sign, most characteristic clinical sign in tricuspid insufficiency, is augumentation of systolic murmur in inspiration. Diagnosis can be made by cardiac catheterization with right ventriculography, but aided by EKG or 2-dimensional contrast echocardiography. Prognosis is variable. Some expire in early infancy due to congestive heart failture, but the others may survive through their adulthood without surgical treatment. A case of isolated congenital tricuspid insufficiency in 1-year 5-months old girl, who complained of intermittent exertional dyspnea and lip cyanosis on severe crying, is presented with a review of related literatures.

Keywords :Isolated congenital tricuspid insufficiency;Carvallo's sign;2-dimensional contrast echocardiography