All issues > Volume 26(8); 1983

Case Report

J Korean Pediatr Soc. 1983;26(8):829-834. Published online August 31, 1983.

A Case of Myelofibrosis.

Ho Seong Yoo¹, Jin Heon Kim¹, Keun Chul Myung¹, Chang Soo Ra¹

¹Department of Pediatrics, College of Medicine，Chosun University

Abstract

Myelofibrosis is characterized by fibrosis of bone marrow, leukoerythrobla stotic anemia and extramedullary hematopoesis with varying degree of hepatosplenomegaly. Idiopathic myelofibrosis is primarily a disease of the adult and is rare in the pediatric age group. We experienced a case of idiopathic myelofibrosis in a 2 year 5 month old male who showed severe anemia with abnormal forms of red blood cell (teardrops, ovalocytes), nucleated red cells, huge splenomegaly and fibrosis of the bone marrow. We presented a case of idiopathic myelofibrosis with brief review of the literatures.

Keywords :Idiopathic myelofibrosis.