All issues > Volume 26(8); 1983

Case Report

J Korean Pediatr Soc. 1983;26(8):823-828. Published online August 31, 1983.

A Case of Sturge-Weber Syndrome.

Jun Taek Park¹, Geom Hyun Jang¹, Jae Kyu Lee¹, Kyu Eun Lee¹, Jung Hyup Oh²

¹Department of Pediatrics, Seoul Adventist Hospital, Seoul, Korea
²Department of Ophthalmology, Seoul Adventist Hospital, Seoul，Korea

Abstract

We experienced a case of Sturge-Weber Syndrome in 6 month old male. The diagnosis was established by charecteristic features of Sturge-Weber Syndrome such as facial port-wine nevus, focal seizure, hemiparesis, glaucoma and typical calcification & brain atrophy as on brain CT. Plain radiographys of the skull revealed no evidence of calcification, But the brain C.T. clearly showed calcific densities. We have presented this case and reviewed the related literature.

Keywords :Sturge-Weber Syndrome; Brain CT