All issues > Volume 26(8); 1983

Original Article

J Korean Pediatr Soc. 1983;26(8):760-769. Published online August 31, 1983.

Absence of Inferior Vena Cava.

Sun Oak Park¹, Chang Yee Hong¹

¹Department of Pediatrics, College of Medicine, Seoul National University

Abstract

Out of 1617 cases of congenital heart disease, who were admitted to the Pediatric ward, Seoul National University Hospital, for cardiac catheterization during recent 5 years, 20 patients with anomalous inferior vena cava were observed. Associated cardiac and extracardiac vascular anomalies were reviewed. Cardiac and visceral malposition were also analyzed. Results; 1) Incidence was 1.2% of total 1617 catheterized patients. 2) Male and female ratio was 8 : 12. 3) Age distribution by 5 years interval was as follows. 0〜5 years; 12 cases;5〜 10 years; 6 cases 10〜 15 years; 2 cases 4) Twelve cases of cardiac and visceral malposition were seen. Asplenia was associated in 4 cases. Dextrocardia with situs inversus: 5 cases** Levocardia with situs inversus or ambiguus: 7 cases** 5) Associated cardiac anomalies; Cyanotic C.H.D. 13 cases Acyanotic C.H.D.; 7 cases Single atrium 5 V.S.D. 5 Cor-biloculare 4 A.S.D. 2 Single ventricle 1 T.G.A. 1 T.O.F. 1 D.O.R.V, 1 6) In 3 cases, right mediastinal mass like shadow was observed. In lateral film, absence of LV.C. shadow below right atrium was recognized in 4 cases. 7) Arrhythmia, including 1 case of coronary sinus rhythm was noted on EKG in 7 cases 8) In 15 cases, the venous drainage was through azygos vein and in 5 cases through hemiazygos vein. 9) Persistent left superior vena cava was associated in 9 cases especially with hemiazygos continuation (4 cases out of 5 patients with hemiazygos continuation). ****; 4 cases of asplenia

Keywords :Absence of I.V.C.; Azygos; Hemiazygos; Malposition, Asplenia; Persistent left S.V.C..