All issues > Volume 26(5); 1983

Case Report

J Korean Pediatr Soc. 1983;26(5):516-520. Published online May 31, 1983.

A Case of Klippel-Trenaunary-Weber Syndrome.

Do Seung Lee¹, Dae Yong Hwang¹, Jeong Sick Min¹, Jae Sun Park¹

¹Department of Pediatrics，Kosin Medical College, Gospel Hospital, Busan, Korea

Abstract

We report a case of Klippel-Trenaunay-Weber Syndrome in a 12 years old boy who had large port-wine hemangioma, soft tissue & bony hypertrophy and varicose veins on the lower leg. On the skin lesion, there are several black papules & crops of skin colored eruptions which were found out microscopically to be intraepidermal bleeding focuses & harmatomatous change of squamous cells into sebaceous cells respectively. In our case, femoral angiography showed no A-V fistula. A brief review of literatures was made.

Keywords :Port-Wine hemangioma; Soft tissue & bony hypertrophy; Varicose vein.