All issues > Volume 26(4); 1983

Case Report

J Korean Pediatr Soc. 1983;26(4):392-396. Published online April 30, 1983.

A Case of Hand Schuller Christian Disease.

Yeon Saeng Lee¹, Soo Young Kim¹, So Kyung Park¹, Dong Hak Shin¹

¹Department of Pediatrics, Keimyung University Medical College and Hospital, Daegu, Korea

Abstract

Hand-Schuller-Christian disease is reactive granulomatous lesion with histiocytic proliferation, the cause of which is unknown. Recently, we experienced a case in a 3 years old female with polydipsia and polyuria. We established the diagnosis with clinical features, radiologic examination and bone biopsy- Histiologic examination of frontal bone showed mild to moderate infiltration of eosinophils， lymphocytes, plasma cells and large histioytes and fibrosis. Similiar cases reported in literature are briefly reviewed.

Keywords :Hand-Schuller-Christian disease; Diabetes insipidus.