All issues > Volume 26(1); 1983

Case Report

J Korean Pediatr Soc. 1983;26(1):66-70. Published online January 31, 1983.

A Case of Omphalocele Associated with Multiple Congenital Anomalies.

Yoon Ja Kim¹, Soo Kyung Jeong¹, Nam Ji Cho¹, Jae Keum Ji²

¹Department of Pediatrics，National Seoul Hospital, Seoul, Korea
²Department of Pathology，College of Medicine，Seoul National University

Abstract

A omphalocele associated with multiple congenital anomalies is extremely rare congenital malformation. We experienced a ruptured large omphalocele of short duration associated with multiple congenital anomalies such as patent omphalomesenteric duct, cleft palate and lip, postaxial polydactylia with dystrophic nails on both hands and leftfoot, adrenal heterotophia in left peritesticular region, pancreatic heterotophia in perisplenic lymphnode, nodular excrescene of spleen, and cystic lymphangioma involving thyroid. A brief case history with autopsy finding and review of literatures were presented.

Keywords :Omphalocele; Multiple congenital anomalies.