All issues > Volume 25(11); 1982

Case Report

J Korean Pediatr Soc. 1982;25(11):1181-1184. Published online November 30, 1982.

A Case of Potter Syndrome.

Young Mi Hong, Hae Seung Kim, Jung Gon Kim, Keun Lee

¹Department of Pediatrics, College of Medicine，Ewha Womans University

Abstract

In 1946 Potter described a series of 20 cases in infants in whom bilateral absence of the kidneys was associated with, hypoplasia of the lung and characteristic face. The main facial features she described were increased space between the eyes, a prominent fold which arises at inner canthus and sweeps downward and laterally below the eyes, unusual flattening of the nose, excessive recession of the chin, moderate enlargement and decreased chondrification of the ear, and suggestion of premature senility. We reported a female neonate diagnosed by autopsy as Potter syndrome which was characterized by bilateral renal agenesis, bilateral pneumothorax and characteristic face.

Keywords :Potter syndrome, pneumothorax, renal agenesis