All issues > Volume 25(9); 1982

Case Report

J Korean Pediatr Soc. 1982;25(9):967-971. Published online September 30, 1982.

A case of lamellar ichthyosis.

Dong Whan Cha, Kwan Sup Chung, Kwang Ho Kim, Duk Hyun Kim

¹Department of Pediatrics、Inchon Christian Hospital

Abstract

One case of rare form of lamellar ichthyosis was reported. On admission, the entire skin surface of this infant was covered with parchment-like membrane especially below both ears and extensor surface of upper arms. Masked face, eversion of both lips and fixed semiflexion attitude of the upper limbs were also noted. Diagnosis of lamellar ichthyosis was made by clinical features, histcpathological and laboratory studies. A brief review of literatures were presented.

Keywords :Lamellar Ichthyosis (skin biopsy, non-pitting edema).