All issues > Volume 25(9); 1982

Case Report

J Korean Pediatr Soc. 1982;25(9):954-958. Published online September 30, 1982.

A case of Letterer-Siwe disease.

H J Suh, E H Kang, K C Han, S K Moon

¹Department of Pediatrics Fatima Hospital, Taegu，Kcrea
²Department of Pathology Fatima Hospital, Taegu，Kcrea

Abstract

A case of Letterer-Siwe disease in a 2 year old boy manifesting such classic signs described by Siwe as, hepatosplenome^aly, swelling of lymph node, bleeding tendency, anemia, fever and bony skull defects is presented. The diagnosis was confirmed by clinical symptoms, laboratory data, histopathologic and radiologic fingings. The authors report a fatal case which was treated in this hospital with review of pertinent literatures.

Keywords :Letterer-Siwe Disease.