All issues > Volume 25(9); 1982

Case Report

J Korean Pediatr Soc. 1982;25(9):945-953. Published online September 30, 1982.

A case of myelofibrosis.

Hae Jung Cho, Keun Chull Choi, Chul Lee, Myong Ho Lee, Sook Ja Park

¹Department of Pediatrics Presbyterian Medical Center, Chonju, Korea
²Department of Clinical Pathology Presbyterian Medical Center, Chonju, Korea

Abstract

The so called “Myelofibrosis” within the category of myeloproliferative disorders consists of various degrees of leukoerythroblatosis, bone marrow fibrosis, and extramedullary hema- topoiesis with hepatosplenomegaly. Primary myelofibrosis occurs predominantly in adults and few in childhood. We experie- nced one case of myelofibrosis, at 17 month old male patient. He was admitted due to intermittent fever, pallor and abdominal distension. On admission, hepatosplenomegaly, anemia and generalized petechia without jaundice was noticed. Leukoerythroblastosis and tear-drop cells were seen in the peripheral blood smear. Bone marrow finding was diagnosed as myelofibrosis. He was discharged without specific treatment. A Brief reviewof related literature is. also presented.

Keywords :Myelofibrosis