All issues > Volume 25(4); 1982

Case Report

J Korean Pediatr Soc. 1982;25(4):393-398. Published online April 30, 1982.

A Case of Polycystic Kidney Associated with Pulmonary Hypoplasin in a Newborn Neonate.

Seong Ky Chung¹, Yoon Bae Lim¹, Ky Yang Ryoo¹, Seong Hoe Park²

¹Dpartment of Pediatrics, Kang Nam Sacred Heart Hospital, Korea.
²Dpartment of Pethology, Kang Nam Sacred Heart Hospital, Korea.

Abstract

Polycstic kidney was rare problem of pediatric disease category. We have experienced one case of polycstic kidney(Potter type I) with pulmonary hypoplasia who born after 35 weeks of gestation to a 34 year-old mother. The clinical course of this infant was characterized by respiratory difficulty with apnea, cyanosis and marked abdominal distension. Chest X-Ray film showed no airation in the both lung fields. He died from respiratory failure due to pulmonary hypoplasia, 3 hrs after birth. We tried discussion about polycstic kidney with literature review.

Keywords :Polycstic kidney with pulmonary hypoplasia;proliferation of bile ducts in liver