All issues > Volume 23(5); 1980

Case Report

J Korean Pediatr Soc. 1980;23(5):417-422. Published online May 15, 1980.

A cases of Congenital Nephrogenic Diabetes Insipidus with Bilateral Hydronprosis.

Young Mo Sohn, Chul Lee, Pyung Kil Kim, Duk Jin Yun

¹Department of Pediatrics, College of Medicize Yonsei University Seoul, Korea.

Abstract

A 13 year old boy was diagnosed as primary nephrotic diabetesinsipidus, whose symptom has been devloped from 3 years of age, subsequetly he developed bilateral hydronephrosis and neurogenic bladder. His pedigree could be explored 5 generations and represented inheritace as X-linked recesslive transmission, He was treated with indomethacin 2mg/Kg/day plus chlorothiazid 500mg/dau and this new method shows markedly decreased urine outpur and increased urine osmolarity.

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