All issues > Volume 23(3); 1980

Case Report

J Korean Pediatr Soc. 1980;23(3):252-256. Published online March 15, 1980.

A Case of Letterer-Siwe Disease.

Gyung Hee Kim, Choong Hee Kim, Keun Lee, Chul Kyu Kim

¹Department of Pediatrics, College of Medicaine, Ewha Womans University, Seoul, Korea.

Abstract

The patient was presented characteristic clinical, histopathological and X-ray findings, in cluding generalized edema, petechial rash, lymphadenopathy, bone lesions, pulmonary infiltration and hepatomegaly with anemia. Most of these signs developed soon after birth. Diagnosis was confirmed by microscopic examin ation of lymph node biopsy and clinical X-ray findings. The patient was received antibiotics, corticosteroid and vinblastine and discharged against doctors order without improvement.

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