All issues > Volume 22(7); 1979

Case Report

J Korean Pediatr Soc. 1979;22(7):546-549. Published online July 15, 1979.

A Case Report of Systemic Mastocytosis.

Kwang Tae Chung¹, Ja hoon Koo¹, Sae Kwang Moon²

¹Department of pediatrics, Kyung Pook National University, School of Medicine, Taegu, Korea.
²Deprtment of Pathology, Fatima hospital, Taegu, Korea.

Abstract

A case of systemic mastocytosis in a 6 year old boy was presented. Skin lesions started to appear and spred several days after birth along with severe itching sensation, and intermitent abdominal pain & constipation developed at the age of 5. On physical examination, he was found to be underdeveloped (Height less than 3rd percentile) with normal vital signs. Liver was felt 1 1/2 fb below costal margin, spleen 2 fb. There were many brown to dark brown-colored irregular shaped maculopapulourticarial skin lesions, scattered all over the body, along with multiple thickened areas, and positive Darier's sign was noted. On upper GI series, many honey-combed filling defect were found throughout small intestine. Skin biopsy confirmed the diagnossis : showing multiple scattered infilteration of mast cells.

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