All issues > Volume 21(9); 1978

Case Report

J Korean Pediatr Soc. 1978;21(9):607-613. Published online September 30, 1978.

A case of total aganglionic intestine.

Ho Seong¹, Su Dong Lee¹, Don Hee Ahn¹, Keun Chan Sohn¹, Hea Soo Koo², Moon Hyang Park²

¹Department of pediatrics, National Medical Center, Korea
²Department of Pathology, National Medical Center, Korea

Abstract

A case of total aganglionic intestine in a new born infant is presented with a review of literature. Persistent vomiting, abdominal distension, failure to pass meconeum since brith were manifested. All X-rays showed multiple fluid level suggesting intestinal obstruction. In spite of colostomy with meticulous medical care, the patient expired due to cachexia. Postmortem autopsy findings were complete abscence of Auerbach's plexuses in entire intestine including esophagus, stomach, small intestine and colon.

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