All issues > Volume 21(2); 1978

Case Report

J Korean Pediatr Soc. 1978;21(2):136-142. Published online February 28, 1978.

A case of Histiocytic Medullary Reticulosis.

Jong Youl Kim¹, Seouk Tak Son¹, Ki Chang Han¹, Young Hae Park¹, Sae Kwang Moon²

¹Department of Pediatrics, Fatima Hospital, Daegu, Korea.
²Department of Pathology, Fatima Hospital, Daegu, Korea.

Abstract

A case of histiocytic medullary reticulosis in 14-years-old girl was presented, who had characteristic clinical and histiopathologic findings. The patient manifested intermitten fever, general weakness, weight loss, multiple skin lesion and pancytopenia with terminal massive bleeding. The clinical finding with fatal course and hematologic features were basically identical to those of previously documented histiocytic medullary reticulosis and verified with autopsy. On autopsy, systemic proliferation of the actively phagocytic atypical histiocytes was found. The authors report the case with review of pertinent literature.

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