All issues > Volume 14(1); 1971

Original Article

J Korean Pediatr Soc. 1971;14(1):1-12. Published online January 31, 1971.

A Clinical Study on Histiocytosis Syndromes: Review of Ten Cases

Y.K. Chang¹, Y.W. Hong¹, B.H. Rie¹, J.Y . Choi¹, C.Y. Hong¹

¹Department of Pediatrics, College of Medicine, Seoul National University

Abstract

Ten cases of Histiocytosis syndromes who had been admitted to Seoul National University Hospital from 1960 to 1968 were reviewed.1. One case belongs to group I, five cases to group II and four cases to group III Sex ratio: male to female was 6 : 4. 2. Age onset ranged from 2. 5 months to five years, average 3. 5 years in group I, 2. 5 years in group II , and 1. 5 years in group III. 3.Only ane case in group I showed the all signs included in. triad exophthalmos, polyuria, and skull defects. 4.Three quarters of patients in group III had dermatitis, hepatosplenomegaly, lymphnode swelling and anemia. 5. A case belongs to group HI showed lung infiltration at the onset. 6. Bone lesions were main characteristic in group I and group II. Calvarial defects in group II revealed in all cases. Prednisone was effective pn bone lesions. 7.All cases in group III died.

Keywords :