All issues > Volume 16(10); 1973

Case Report

J Korean Pediatr Soc. 1973;16(10):772-776. Published online October 31, 1973.

A Case of Pheochromocytoma

Sai Youn Oh¹, Byung Hae Yoon¹, Keun Chan Sohn¹, Keun Soo Lee¹, Chui Sang Lee², Do Hun Rha², Kie Chung Kim³

¹Department of Pediatrics,National Medical Center Seoul, Korea
²Department of General Surgery,National Medical Center Seoul, Korea
³Department of Radiology, National Medical Center Seoul, Korea

Abstract

Pheochromocytoma is a rare tumor arising from chromaffin cells of the sympatho-adrenal system which produce large amount of epinephrine and nor-epinephrine. Recently a 8year old male patient. was admitted to our Pediatric Department of National Medical Center who had suffered from sweating, polyuria polydipsia and palpitation for 3 years and hypertension was found 3 months ago, which persisted till this admission. In urine examinations, proteinuria was sustained but not glycosuria. Urinary excretion of catecholamine was markedly increased and VMA was also increased in 24 hours urine but not'so marked as catecholamine. Regitine test was positive but histamine test and BMR were not performed. Retroperitoneal pneumography showed adult-thumb tip sized soft tissue mass locating at just above the upper pole of right kidnay, which was highly suggestive of rich vascular adrenal tumor by abdominal aortography. Right adrenalectomy was performed by surgical department. Blood pressure was stabilized after 36 hours-operation and tumor was confirmed as pheochromocytoma by histopathological study. Two weeks after operation, he was discharged with good general condition and we report this case with review of literatures.

Keywords :