All issues > Volume 15(10); 1972

Original Article

J Korean Pediatr Soc. 1972;15(10):944-950. Published online October 31, 1972.

Clinical Review of Progressive Muscular Dystrophy

Shin Hyung Chang¹, Ze Bo Cho¹, Ji Sub Oh¹, Dong Hyuk Kim¹, Dong Hak Shin¹

¹Department of Pediatrics, Presbyterian Hospital Taegu, Korea

Abstract

The authors has observed 19 patients of progressive muscular dystrophy who were admitted to the Pediatric department and Orthopedic department and diagnosed by clinical symptoms, urine findings and muscle biopsy during the period from Mar. 1960 to April 1971. The results are as follows: 1) The most common form was Dechenne type (84.1%) and 2) All cases were male 3) In Duchenne type, the case of onset under 5 years old was 9 cases (56.25%) 4) Urinary creatine excretion was decreased, while urinary creatine value was elevated and so urinary creatine-creatinine ratio was decreased. 5) In Duchenne type, mental retardation was noted in 4 cases (25%).

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