All issues > Volume 11(2); 1968

Case Report

J Korean Pediatr Soc. 1968;11(2):95-100. Published online February 28, 1968.

Persistent Ostium Atrioventriculare Commune(Report of a Case Associated with Multiple Anomalies of Viscera)

Jae Hak Seo¹, Yong II Lee¹, Han Woong Choi¹, Je G. Chi², Sang In Kim²

¹Department of Pediatrics, Han II Hospital
²Department of Pathology, College of Medicine, Seoul National University Seoul, Korea

Abstract

This 1.8 kg-weighing premature male baby was admitted to the department of Pediatrics, Han II Hospital through emergency room because of high fever, dyspnea and peripheral cyanosis on Sept. 31, 1965. This baby was spontaneously delivered on 34 weeks of gestation. Initial crying and disappearance of cyanosis after birth were not delayed. But his parents noticed the difficulty of respiration and high fever from 3 hours of his life. General condition was aggravated gradually and progressively thereafter, and the patient expired at the 16th hours after birth. At autopsy a rare congenital heart malformation, persistent ostium atrioventriculare commune, that was associated with multiple other anomalies of the viscera, i.e., tracheo-esophageal fistula, horseshoe kidney with triple ureters, rectal and anal atresia were observed. The common atrioventricular canal was complicated with interatrial septal defect of ostium secundum type. Tracheo-esophageal fistula was that o£ type C. Anal atresia was that of type 3. Both kidneys fused together at the mid line of the body and the right-sided kidney showed double pelves and ureters crossing the anterior surfaces to reach the bladder. The direct cause of death was extensive bilateral bronchopneumonia.

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