| An Autopsy Case of Infant of Diabetic Mother with d-Transposition of Great Arteries and Hypertrophic Cardiomyopathy |
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Kye Hwan Seol, Eui Kyeung Jung, Chang Sung Son, Joo Won Lee, Soon Kyum Kim |
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Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea |
| 당뇨병 모체에서 태어난 신생아에서의 비후성 심근증을 동반한 대혈관 전위증 부검 1례 |
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설계환, 정의경, 손창성, 이주원, 김순겸 |
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고려대학교 의과대학 소아과학교실 |
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| Abstract |
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Generally, infants of diabetic mother(IDM) have various diseases and complications affecting multisystems resulting in high perinatal morbidity and mortality. It is well known that IDM have especially higher incidence of congenital anomalies including congenital heart disease(CH D). dTransposition of great arteries(d-TGA), ventricular septal defect and hypertrophic cardiomyopathy(HCM) form most of CHD occurring in IDM. Of these, HCM appears as a benign, transient and nonfamilial cardiomyopathy in early neonatal period with the natural history of a spontaneous resolution of symptoms and septal hypertrophy. Most of IDM with HCM need only supportive care, whereas those with d-TGA show high mortality despite of intensive care. Recently the authors experienced 1 case of a female newborn with congenital heart disease who was delivered to a diabetic woman by cesarean section with birth weight 4800gm and expired 12 hours after birth. So we report this case of IDM accompanying hypertrophic cardiomyopathy and d-TGA which were confirmed on autopsy, with a brief review of literatures. |
| Key Words:
Infants of diabetic mother, Hypertrophic cardiomyopathy, d-TGA |
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