Two Case of Dyke-Davidoff-Masson Syndrome |
Dong Gun Park, Ji Hee Park, Kee Hwan Yoo, Ji Tae Choung, Chang Sung Son, Young Chang Tockgo |
Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea |
Dyke-Davidoff-Masson증후군 2례 |
박동건, 박지희, 유기환, 정지태, 손창성, 독고영창 |
고려대학교 의과대학 소아과학교실 |
|
|
Abstract |
Dyke-Davidoff Masson syndrome is a rare disorder which developed hemiatrophy of brain, enlargement of ventricles and prominet pneumatrization of pertous pyramid of the temporal bone. It manifests hemiparesis, varying type seizure, and mental retardation.
We experienced two cases of Dyke-Davidoff-Masson Syndrome, in a 6/12 year-old boy and a 1,10/12 year-old girl who were admitted to our department of pediatrics, because of convulsion and hemiparesis
The brain CT sean showed marked dilatation of lateral ventricle, prominent sylvian fissure and cortical sulci.
So we report two cases of Dyke-Davidoff-Masson syndrome with review of lierature. |
Key Words:
Cerebral hemiatrophy, Hemiparesis |
|